Category: Neuroendocrine Tumors (209)

  • (258.01-258.03) First code any associated multiple endocrine neoplasia syndromes
  • Use additional code to identify any associated endocrine syndrome such as:
    • (259.2) Carcinoid Syndrome
    • excludes: (157.4) Pancreatic Islet Cell Tumors

Subcategories

Malignant Carcinoid Tumors of the Small Intestines 209.0
Malignant Carcinoid Tumors of the Appendix, Large Intestine, and Rectum 209.1
Malignant Carcinoid Tumors of Other and Unspecified Sites 209.2
Malignant Poorly Differentiated Neuroendocrine Tumors 209.3
Benign Carcinoid Tumors of the Small Intestine 209.4
Benign Carcinoid Tumors of the Appendix, Large Intestine, and Rectum 209.5
Benign Carcinoid Tumors of Other and Unspecified Sites 209.6
Secondary Neuroendocrine Tumors 209.7
Neoplasms and Carcinomas

Malignant Carcinoid Tumors of the Small Intestines (209.0)

  • (209.0) Malignant carcinoid tumors of the small intestine
  • (209.00) Malignant carcinoid tumor of the small intestine, unspecified portion
  • (209.01) Malignant carcinoid tumor of the duodenum
  • (209.02) Malignant carcinoid tumor of the jejunum
  • (209.03) Malignant carcinoid tumor of the ileum

Malignant Carcinoid Tumors of the Appendix, Large Intestine, and Rectum (209.1)

  • (209.10) Malignant carcinoid tumor of the large intestine, unspecified portion
  • (209.11) Malignant carcinoid tumor of the appendix
  • (209.12) Malignant carcinoid tumor of the cecum
  • (209.13) Malignant carcinoid tumor of the ascending colon
  • (209.14) Malignant carcinoid tumor of the transverse colon
  • (209.15) Malignant carcinoid tumor of the descending colon
  • (209.16) Malignant carcinoid tumor of the sigmoid colon
  • (209.17) Malignant carcinoid tumor of the rectum

Malignant Carcinoid Tumors of Other and Unspecified Sites (209.2)

  • (209.20) Malignant carcinoid tumor of unknown primary site
  • (209.21) Malignant carcinoid tumor of the bronchus and lung
  • (209.22) Malignant carcinoid tumor of the thymus
  • (209.23) Malignant carcinoid tumor of the stomach
  • (209.24) Malignant carcinoid tumor of the kidney
  • (209.25) Malignant carcinoid tumor of the foregut NOS
  • (209.26) Malignant carcinoid tumor of the midgut NOS
  • (209.27) Malignant carcinoid tumor of the hindgut NOS
  • (209.29) Malignant carcinoid tumors of other sites

Malignant Poorly Differentiated Neuroendocrine Tumors (209.3)

  • (209.30) Malignant poorly differentiated neuroendocrine carcinoma
  • (209.31) Merkel cell carcinoma of the face
  • (209.32) Merkel cell carcinoma of the scalp and neck
  • (209.33) Merkel cell carcinoma of the upper limb
  • (209.34) Merkel cell carcinoma of the lower limb
  • (209.35) Merkel cell carcinoma of the trunk
  • (209.36) Merkel cell carcinoma of other sites

Benign Carcinoid Tumors of the Small Intestine (209.4)

  • (209.40) Benign carcinoid tumor of the small intestine, unspecified portion
  • (209.41) Benign carcinoid tumor of the duodenum
  • (209.42) Benign carcinoid tumor of the jejunum
  • (209.43) Benign carcinoid tumor of the ileum

Benign Carcinoid Tumors of the Appendix, Large Intestine, and Rectum (209.5)

  • (209.50) Benign carcinoid tumor of the large intestine, unspecified portion
  • (209.51) Benign carcinoid tumor of the appendix
  • (209.52) Benign carcinoid tumor of the cecum
  • (209.53) Benign carcinoid tumor of the ascending colon
  • (209.54) Benign carcinoid tumor of the transverse colon
  • (209.55) Benign carcinoid tumor of the descending colon
  • (209.56) Benign carcinoid tumor of the sigmoid colon
  • (209.57) Benign carcinoid tumor of the rectum

Benign Carcinoid Tumors of Other and Unspecified Sites (209.6)

  • (209.60) Benign carcinoid tumor of unknown primary site 
  • (209.61) Benign carcinoid tumor of the bronchus and lung
  • (209.62) Benign carcinoid tumor of the thymus
  • (209.63) Benign carcinoid tumor of the stomach
  • (209.64) Benign carcinoid tumor of the kidney
  • (209.65) Benign carcinoid tumor of the foregut, not otherwise specified (NOS)
  • (209.66) Benign carcinoid tumor of the midgut, NOS
  • (209.67) Benign carcinoid tumor of the hindgut, NOS
  • (209.69) Benign carcinoid tumors of other sites

Secondary Neuroendocrine Tumors (209.7)

  • (209.70) Secondary neuroendocrine tumor, unspecified site
  • (209.71) Secondary neuroendocrine tumor of distant lymph nodes
  • (209.72) Secondary neuroendocrine tumor of liver
  • (209.73) Secondary neuroendocrine tumor of bone
  • (209.74) Secondary neuroendocrine tumor of peritoneum
  • (209.75) Secondary Merkel cell carcinoma
  • (209.79) Secondary neuroendocrine tumor of other sites

Neoplasms & Carcinomas

Benign Neoplasm of Other Parts of Digestive System (211)
  • (211.1) Stomach
    • excludes: benign carcinoid tumors of the stomach (209.63)
  • (211.2) Duodenum, jejunum, and ileum
    • excludes: benign carcinoid tumors of the small intestine (209.40-209.43)
  • (211.3) Colon
    • excludes: benign carcinoid tumors of the large intestine (209.50-209.56)
  • (211.4) Rectum and anal canal
    • excludes: benign carcinoid tumors of the rectum (209.57)
Benign Neoplasm of Respiratory and Intrathoracic Organs (212)
  • ( 212.3) Bronchus and lung
    • excludes: benign carcinoid tumors of bronchus and lung (209.61)
  • (212.6) Thymus
    • excludes: benign carcinoid tumors of thymus (209.62)
Benign Neoplasm of Kidney and Other Urinary Organs (223)
  • (223.0)Benign neoplasm of kidney (except pelvis)
    • excludes: Benign carcinoid tumors of kidney (209.64)
Carcinoma in Situ of Ski (232)
  • excludes: Melanoma in situ of skin (172.0-172.9) 
Carcinoma in Situ of Breast and Genitourinary System (233)
  • (233.1) Carcinoma in situ of cervix uteri
Neoplasm of Uncertain Behavior of Other and Unspecified Sites and Tissues (238)
  • (238.7) Other lymph hematopoietic tissues
  • (238.77) Post-transplant lymphoproliferative disorder (PTLD)
    • Code first complications of transplant (996.80-996.89)